Acute Edema Blisters on a Skin Swelling: An Unusual Manifestation of Hereditary Angioedema
نویسندگان
چکیده
منابع مشابه
Hereditary angioedema: a bradykinin-mediated swelling disorder.
Edema is tissue swelling and is a common symptom in a variety of diseases. Edema form due to accumulation of fluids, either through reduced drainage or increased vascular permeability. There are multiple vascular signalling pathways that regulate vessel permeability. An important mediator that increases vascular leak is the peptide hormone bradykinin, which is the principal agent in the swellin...
متن کاملManagement of upper airway edema caused by hereditary angioedema
Hereditary angioedema is a rare disorder with a genetic background involving mutations in the genes encoding C1-INH and of factor XII. Its etiology is unknown in a proportion of cases. Recurrent edema formation may involve the subcutis and the submucosa - the latter can produce obstruction in the upper airways and thereby lead to life-threatening asphyxia. This is the reason for the high, 30-to...
متن کاملHereditary Angioedema Presenting as Recurrent Acute Pancreatitis.
Hereditary angioedema (HAE) may manifest with swelling of the face, extremities, and upper airways. Gastrointestinal symptoms are also common and may include abdominal pain, vomiting, and diarrhea. However, pancreatic involvement is rare and has been reported only in a few adults with previously diagnosed HAE. We describe a 6-year-old boy who presented with recurrent severe abdominal pain accom...
متن کاملPediatric hereditary angioedema: an update
Hereditary angioedema (HAE) with C1-inhibitor (C1-Inh) deficiency (C1-Inh-HAE) is a rare, life-threatening, and disabling genetic disorder characterized by self-limited tissue swelling caused by deficiency or dysfunction of C1-Inh. Our aim in this update is to discuss new advances in HAE therapy, focusing mainly on the various treatment options that have become available recently and also drugs...
متن کاملAcute isolated uvula swelling: A rare manifestation in patients with COVID-19
Acute and isolated inflammation of the uvula is one of the rare manifestations of COVID-19 virus. In this article, we have introduced two definite cases of this disease without significant pulmonary manifestations. Causes of acute and isolated swelling of the uvula include bacterial infections, viral infections, angioedema, direct mechanical trauma to the uvula - some systemic and inhaled drugs...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: Acta Dermato Venereologica
سال: 2016
ISSN: 0001-5555
DOI: 10.2340/00015555-2252